phenylalanine hydroxylase中文是什么意思
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用"phenylalanine hydroxylase"造句"phenylalanine hydroxylase"怎么读"phenylalanine hydroxylase" in a sentence
中文翻译手机版
- 苯丙氨酸羟化酶
- "phenylalanine"中文翻译 n. 【化学】苯基丙胺酸。
- "phenylalanine 4-hydroxylase" 中文翻译 : 苯丙氨酸4-羟化酶
- "phenylalanine hydroxylase deficiency" 中文翻译 : 苯丙氨酸羟化酶缺乏症,苯丙酮尿症,苯丙氨酸羟化酶缺乏; 苯丙酮尿症
- "phenylalanine" 中文翻译 : n. 【化学】苯基丙胺酸。
- "hydroxylase" 中文翻译 : 氢氧酶; 羟化酶; 羟基化酶
- "benzyloxycarbonyl phenylalanine" 中文翻译 : 下氧基碳酰苯丙氨酸
- "d-phenylalanine" 中文翻译 : 苯丙氨酸
- "dimethyl-phenylalanine" 中文翻译 : 二甲基-苯丙氨酸
- "hydroxymethyl phenylalanine" 中文翻译 : 羟甲基苯丙氨酸
- "isopropyl-phenylalanine" 中文翻译 : 异丙基-苯丙氨酸
- "l phenylalanine" 中文翻译 : 鸟氨酸盐酸盐
- "l-phenylalanine" 中文翻译 : 苯丙氨酸; 苯基丙氨酸
- "nitro phenylalanine" 中文翻译 : 硝基苯基丙氨酸
- "phe-phenylalanine" 中文翻译 : 苯丙氨酸
- "phenylalanine acetyltransferase" 中文翻译 : 苯丙氨酸乙酰转移酶
- "phenylalanine agar" 中文翻译 : 苯丙氨酸琼脂
- "phenylalanine aminotransferase" 中文翻译 : 苯丙氨酸氨基转移酶
- "phenylalanine and methotrexate" 中文翻译 : 苯丙氨酸和氨甲蝶呤
- "phenylalanine deaminase" 中文翻译 : 苯丙氨酸脱氨酶
- "phenylalanine decarboxylase" 中文翻译 : 苯丙氨酸脱羧酶
- "phenylalanine measurement" 中文翻译 : 苯丙氨酸测量
- "phenylalanine monooxygenase" 中文翻译 : 苯丙氨酸单加氧酶; 苯丙氨酸加单氧酶
- "phenylalanine mustard" 中文翻译 : 苯丙氨酸氮芥; 苯基丙氨酸氮芥, 溶肉瘤素
- "phenylalanine nitrogenmustard" 中文翻译 : 苯丙氨酸氮芥
- "pyridoxylidene phenylalanine" 中文翻译 : 吡哆苯丙氨酸
例句与用法
- Phenylketonuria ( pku ) is an inherited metabolic disease that results in mental retardation and other neurological problems when treatment is not started within the first few weeks of life . the disease arises from the deficiency of a single enzyme , phenylalanine hydroxylase , which converts the essential amino acid , phenylalanine , to another amino acid , tyrosine . failure of the conversion to take place results in a buildup of phenylalanine in the body that then damages the central nervous system
苯丙酮尿症( pku )是一种智力发育不全的先天性疾病,患者由于肝赃内苯丙氨酸羟化酶缺乏,苯丙氨酸不能正常代谢为酪氨酸,从而导致苯丙氨酸在肌体组织内积累,引起脑损伤和累进性精神障碍,临床表现为智力低下,头发颜色转黄,尿有异臭味,重者似鼠臭。
其他语种
- phenylalanine hydroxylase 意味
- phenylalanine hydroxylase meaning
- phenylalanine hydroxylase en francais
- phenylalanine hydroxylaseとは意味フェニルアラニン水酸化酵素{すいさんか こうそ}[ヒドロキシラーゼ]
百科解释
Phenylalanine hydroxylase (PheOH, alternatively PheH or PAH) () is an enzyme that catalyzes the hydroxylation of the aromatic side-chain of phenylalanine to generate tyrosine. PheOH is one of three members of the pterin-dependent amino acid hydroxylases, a class of monooxygenase that uses tetrahydrobiopterin (BH4, a pteridine cofactor) and a non-heme iron for catalysis.
详细百科解释
相关词汇
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